Challenges in identifying paediatric cancer predisposition syndromes: international SCOPE survey and SIOPE expert consensus recommendations.

  • Reading time:2 mins read

Journal: European journal of human genetics : EJHG

This publication reports the SCOPE study, a three-part cross-sectional survey and Delphi consensus process focused on cancer predisposition syndromes (CPS) in paediatric oncology across Europe.

Key design points:

  • Participants: 185 paediatric haematology/oncology professionals from 22 European countries.
  • Methods:
    • Survey of clinicians’ confidence, practices, and perceived barriers regarding CPS identification and management.
    • Modified Delphi process with SIOP Europe Host Genome Working Group members to formulate consensus recommendations.

Major findings:

  • Confidence gaps:
    • Over 40% of clinicians reported low or uncertain confidence in multiple CPS-related tasks.
    • Confidence was particularly low for:
      • Counselling families about CPS (64.3% low/uncertain).
      • Interpreting germline genetic findings (57.3% low/uncertain).
  • Determinants of confidence:
    • Better access to clinical geneticists and dedicated CPS clinics was associated with higher confidence.
    • Individual experience and institutional patient volume had limited impact.
  • Screening practices:
    • Regular use of universal CPS screening tools was uncommon (42.3%).
    • Most clinicians relied on individual clinical judgement rather than structured criteria.
  • Perceived barriers:
    • Lack of clear CPS screening guidelines (57%).
    • Difficulty interpreting genetic test results (35.1%).

Identified needs:

  • More regular CPS-focused training and workshops for clinicians.
  • Availability of genetic counsellors or dedicated educators to support patients and families.
  • Patient-friendly, accessible educational materials on CPS.

Consensus recommendations from the Delphi process:

  1. Enhance clinician training and communication skills specific to CPS.
  2. Integrate CPS screening systematically into standard paediatric oncology treatment pathways.
  3. Develop and disseminate accessible, patient-centred educational resources on CPS.

Overall, the study underscores substantial unmet needs in CPS recognition and management in paediatric oncology and provides clear, consensus-based priorities to improve practice through structured screening, specialist support, and better education.

Leave a Reply